منابع مشابه
Isolated pulmonary histiocytosis.
Pulmonary disease in the 'histiocytosis syndromes' is not uncommon. Isolated pulmonary histiocytosis, however, is rarely diagnosed. We describe three patients with this condition, with ages ranging from 3 weeks to 9 1/2 years, in whom there was no evidence of disease in any other organ. Their presentation, treatment, and clinical progress over three years of follow up are discussed.
متن کاملIsolated Pulmonary Langerhans-Cell Histiocytosis Mimicking Miliary Tuberculosis
11 Abstract Isolated involvement of lungs in the course of Langerhans'-cell histiocytosis (LCH) is very rare in childhood. Spontaneous pneumothorax (PTX) may occur during the course which necessitates rapid intervention. We present a 17 months-old girl who was sent with the pre-diagnosis of miliary tuberculosis. Despite antituberculosis therapy, her pulmonary function deteriorated. The chest to...
متن کاملPrimary pulmonary histiocytosis X.
During the past 40 years, three previously unrecognized disorders of the reticuloendothelial system have been described : Letterer-Siwe’s disease,’ Hand-Sch#{252}ller-Christian’s disease,24 and eosinophilic granuloma.5’6 Due largely to the influence of Lichtenstein,7 the opinion now prevails that these three disorders are fundamentally related. They differ from one another mainly in terms of pa...
متن کاملPulmonary langerhans cell histiocytosis
Pulmonary Langerhans' cell histiocytosis (PLCH) remains an important diagnostic consideration in the differential diagnosis of diffuse infiltrative lung disease, particular among smokers. This review highlights recent progress in our understanding of the etiology, clinical presentation, and diagnostic and therapeutic approaches to this unusual lung disorder. Evolving studies strongly link the b...
متن کاملPulmonary Langerhans cell Histiocytosis.
Pulmonary Langerhans cell Histiocytosis is a rare granulomatous disease affecting both sexes, with greater incidence in the second and third decades of life; smoking appears to be the most important risk factor. Its etiology is unknown, although there are data indicating an uncontrolled immune response as possible cause, sustained by the Langerhans cells, antigen presenting cells for T lymphocy...
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ژورنال
عنوان ژورنال: Archives of Disease in Childhood
سال: 1989
ISSN: 0003-9888,1468-2044
DOI: 10.1136/adc.64.1.178-a